The esophageal atresia is a group of birth defects including a break in continuity of the
esophagus with or without persistent communication with the trachea (tracheoesophageal
fistula), sometimes associated (from 50%) of other malformations (heart, kidney, digestive
The current prognosis for this ailment is good. However he persists a mortality (<10%) and
significant morbidity, firstly related malformations (heart, kidney, for example), and
secondly with particularly difficult anatomical forms (Forms long defect) .
The prevalence of this condition is estimated to be 1/2500 in 3000 live births, making an
estimated ± 2,500 new cases over to 10 years in France.
The current project aims to set up a national registry (Metropolitan France and Dom Tom) to
measure the prevalence of esophageal atresia among live births, phenotypic characteristics,
the circumstances of their diagnosis, and their initial future at short-term during the first
year of life, at which time occurs the vast majority of deaths and complications in this